Download (Article 09 – Volume 23 – Issue 3)

Autosomal Recessive Rough Hypoplastic Type-1 Amelogenesis Imperfecta
Uzma Shahbaz1 , Fauzia Quadir2 , Tasleem Hosein3

1. Assistant Professor Department of Operative Dentistry Fatima Jinnah Dental College, Karachi.
2. Assistant Professor Department of Operative Dentistry Dow Dental College, Karachi.
3. Professor and Dean Fatima Jinnah Dental College, Karachi. < hosein.tasleem@gmail.com >
Corresponding author: “Dr Fauzia Qadir” < fzb80@hotmail.com >

Volume 23, Issue 3 (July - September 2014)

Open Access

ABSTRACT:

Amelogenesis Imperfecta (AI) is a severe disorder affecting patient’s quality of life with relation to their oral health and may have serious psychological impact on them. From this point of view, people with AI need extensive treatment. While planning the treatment, several factors must be taken into account like patient’s age, their affordability, pattern and the nature of AI. Moreover, although rare, some dental anomalies may accompany the AI cases.

This case report presents restorative management of an Autosomal Recessive Rough Hypoplastic AI. The patient was looking for a cost effective solution of her aesthetic problem and replacement of her missing teeth. The management of her case involved direct and indirect restorations. Contemporary treatment modalities comprising of adhesive restorative techniques, removable partial dentures and stainless steel metal crowns were used in this case report. Patient reported her comfort with the restorative treatment on her follow up visits. HOW TO CITE: Shahbaz U, Quadir F, Hosein T . Autosomal Recessive Rough Hypoplastic Type-1 Amelogenesis Imperfecta. J Pak Dent Assoc 2014; 23(3):131-135